Pigmented progressive purpuric dermatosis
https://en.wikipedia.org/wiki/Pigmented_purpuric_dermatosis
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Schamberg disease ― un home de 26 anos cunha mancha de pigmentación asintomática e telangiectasia na perna.
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References
Pigmented Purpuric Dermatoses: A Complete Narrative Review 34070260 NIH
Pigmented purpuric dermatoses (PPD) son un grupo de afeccións cutáneas marcadas por pequenas áreas de sangrado baixo a pel debido á inflamación dos capilares. A PPD adoita comezar como manchas vermellas a violetas que posteriormente se tornan douradas a medida que se reabsorbe a hemosiderina.
Pigmented purpuric dermatoses (PPD) include several skin diseases characterized by multiple petechial hemorrhage as consequence of capillaritis. PPD generally present with red to purple macules that progressively evolve to golden-brown color as the hemosiderin is reabsorbed.
Schamberg Disease 32809367 NIH
Schamberg disease é o tipo máis común de pigmented purpuric dermatoses (PPDs) , que son afeccións crónicas da pel caracterizadas por pequenas manchas vermellas ou roxas e un aumento da cor da pel (parches de cor marrón, vermella ou amarela) . Os PPD clasifícanse en cinco tipos: Schamberg's purpura, Majocchi purpura, lichen aureus, Gougerot-Blum purpura, eczematoid-like purpura of Doucas and Kapetanakis. Schamberg disease (SD) tamén se coñece como progressive pigmentary dermatosis of Schamberg, purpura pigmentosa progressiva, Schamberg's purpura. Afecta principalmente aos machos e normalmente aparece na parte inferior das pernas, pero tamén pode ocorrer nas coxas, nádegas, tronco ou brazos.
Schamberg disease represents the most common type of pigmented purpuric dermatoses (PPDs), a chronic, benign, cutaneous eruptions characterized by petechiae, purpura, and increased skin pigmentation (brown, red, or yellow patchy). The PPDs are grouped into five clinical entities: Schamberg's purpura, Majocchi purpura, lichen aureus, Gougerot-Blum purpura and, eczematoid-like purpura of Doucas and Kapetanakis. Schamber disease (SD) has also been called: progressive pigmentary dermatosis of Schamberg, purpura pigmentosa progressive and, Schamberg's purpura. It is commonly seen in males and mainly affects the tibial regions, and could involve thighs, buttocks, trunk, or upper extremities.
Characteristics and Clinical Manifestations of Pigmented Purpuric Dermatosis 26273156 NIH
Analizouse a información de 113 pacientes con PPD, incluíndo 38 aos que se someteron a biopsia cutánea para este estudo. O tipo clínico máis frecuente foi a enfermidade de Schamberg (60,5%) . Outras condicións xunto á PPD foron hipertensión (15,8%) , diabetes (10,5%) e outras. Os historiais de medicamentos revelaron estatinas (13,2%) , bloqueadores beta (10,5%) e outros. Os posibles factores relacionados coa PPD incluíron unha infección recente das vías respiratorias superiores (5,3%) , a permanencia prolongada de pé que provoca unha presión ortostática alta (2,6%) e o exercicio intenso (2,6%) . O tratamento foi administrado a 36 pacientes (94,7%) - oral antihistamines, pentoxifylline, topical steroids, and/or phototherapy.
Information on 113 patients with PPD was analyzed, and 38 subjects with skin biopsy were included for this study. Schamberg's disease was the most frequent clinical type (60.5%). Concomitant diseases included hypertension (15.8%), diabetes (10.5%), and others. Associated medication histories included statins (13.2%), beta blockers (10.5%), and others. Possibly associated etiologic factors were recent upper respiratory infection (5.3%), high orthostatic pressure due to prolonged standing (2.6%), and strenuous exercise (2.6%). A total of 36 patients (94.7%) were treated with one or more treatment methods, including oral antihistamines, pentoxifylline, topical steroids, and/or phototherapy.
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